Beh et*s disease presenting with Budd每Chiari syndrome and intracardial thrombus: a case report

作者:Kim MJ; Jo YS; Kim JH; Kim YJ; Kim KH; Lee EB; Song YW; Lee EY
来源:International Medical Case Reports Journal, 2011.
DOI:http://dx.doi.org/10.2147/IMCRJ.S24021

摘要

eh et*s disease presenting with Budd每Chiari syndrome and intracardial thrombus: a case report Case report (2300) Total Article Views Authors: Kim MJ, Jo YS, Kim JH, Kim YJ, Kim KH, Lee EB, Song YW, Lee EY Published Date November 2011 Volume 2011:4 Pages 67 - 71 DOI: http://dx.doi.org/10.2147/IMCRJ.S24021 Minji Jennifer Kim1, Yong Suk Jo2, Jee Hyun Kim2, Yong-Jin Kim3, Kyung Hwan Kim4, Eun Bong Lee2, Yeong Wook Song2, Eun Young Lee2 1School of Medicine, University of Manchester, Manchester, UK; 2Division of Rheumatology, 3Division of Cardiology, Department of Internal Medicine, 4Department of Thoracic Surgery, Seoul National University College of Medicine, Seoul, Republic of Korea Abstract: Budd每Chiari syndrome has been described as a late complication of Beh et*s disease. Although the mortality rate associated with Beh et*s disease is low, it can escalate in the presence of Budd每Chiari syndrome and may be further complicated by intracardial thrombus formation. It is therefore important to detect and initiate management early in the disease course. The imaging modalities of choice should be minimally invasive as certain procedures may aggravate Beh et*s disease by initiating a thrombosis or aggravating an existing one. In Beh et*s disease-induced Budd每Chiari syndrome, cardiac investigation is crucial in the work-up in order to identify any cardiac involvement and determine the etiology of intracardial thrombus. Furthermore, the treatment should ultimately focus on controlling the activity of Beh et*s disease. We report an unusual case of Beh et*s disease presenting with Budd每Chiari syndrome complicated by intracardial thrombus in a young Korean man.

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