Amiloidose traqueobrˋnquica prim芍ria

作者:Chatkin; Gustavo; Pipkin; Maurico; Pinto; Jose Antonio Figueiredo; Silva; Vinicius Duval da; Chatkin; Jose Miguel
来源:Jornal Brasileiro de Pneumologia, 2008.
DOI:10.1590/S1806-37132008000700013

摘要

amyloidosis is a disease characterized by extracellular deposition of fibrillar protein in organs and tissues. primary tracheal amyloidosis is rare. we report here a case of a 55-year-old man with tracheal amyloidosis hospitalized for acute respiratory insufficiency and with a history of recent episodes of pneumonia. chest x-ray and chest computed tomography showed tracheal obstruction due to a tumor. a passage was created in order to relieve the symptoms. histological examination (congo red staining) revealed amyloid deposits but no evidence of neoplasia. although this is a rare clinical condition, its importance is discussed regarding the differential diagnosis of tracheal tumors and the repercussions for therapeutic decision-making.

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