摘要

objective: to study correlations among pulmonary function, chest radiology and clinical status in cystic fibrosis. methods: a retrospective cross-sectional study was performed to evaluate chest x-rays and clinical charts of patients treated at the hospital de cl赤nicas de porto alegre. spirometry findings, shwachman-kulczycki (s-k) scores and brasfield scores were analyzed. results: the final sample consisted of 40 patients (mean age 9.72 ㊣ 3.27). the following mean s-k scores were obtained: total, 80.87 ㊣ 10.24; general activity, 24.75 ㊣ 1.1; physical examination, 18.87 ㊣ 4.59; nutrition, 21.87 ㊣ 4.18; radiology, 15.37 ㊣ 5.23. the mean brasfield score was 18.2 ㊣ 4. the pulmonary function test results, in percentage of predicted, were as follows: forced vital capacity (fvc), 82.99 ㊣ 14.36%; forced expiratory volume in one second (fev1), 83.62 ㊣ 18.26%; and forced expiratory flow between 25 and 75% of fvc (fef25-75), 74.63 ㊣ 2.53%. the s-k score correlated moderately with fvc, whereas it correlated strongly with fev1 and fef25-75. the brasfield score correlated strongly with the s-k total and radiology score, whereas it correlated moderately with pulmonary function. physical examination correlated moderately with fvc, fev1 and fef25-75; as did nutrition with fef25-75; and radiology with fev1 and fef25-75. general activity was the domain that had the greatest influence on the total s-k score. conclusions: these two scoring systems are complementary, correlating with each other, as well as with pulmonary function tests. the radiology domain of the s-k scoring system is a good alternative to the brasfield score.

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