科研之友
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摘要
desmoplastic small round cell tumor (dsrct) is a rare and highly aggressive neoplasm, which predominantly affects young males. we report a case of dsrct affecting an 11-year-old male patient, with intra-abdominal involvement characterized by a large retroperitoneal mass in left hypochondrium. histological examination of the mass showed the presence of clusters of small blue round tumor cells surrounded by a dense desmoplastic stroma. immunohistochemical analysis disclosed a positive reaction to desmin, wt-1 and cytokeratins. after diagnosis, the patient underwent chemo radiotherapy treatment, but died at the 24th month of follow-up.
