Dermatose perfurante adquirida associada 角 insufici那ncia hep芍tica em paciente transplantado de f赤gado

作者：Badziak; Daniela; Lenhardt; Carolina; Barros; Michele F de; Mandelli; Fernando Luiz; Serafini; Sergio Zueda; Santamaria; Jesus Rodriguez

来源：Anais Brasileiros de Dermatologia, 2007.

DOI：10.1590/S0365-05962007000100007

• cholestasis
• folliculitis
• glycogen storage disease type i
• keratin
• liver failure
• liver transplantation
• pruritus.

acquired perforating dermatosis is characterized by transepithelial elimination of degenerated dermal substances. it occurs in many conditions, such as: diabetes mellitus, chronic renal failure and sclerosing cholangitis. this article describes a 17-year-old caucasian female with type i glucogenosis and acquired perforating dermatosis due to chronic hepatic failure caused by hepatic complication of liver transplant.