Mastocitose bolhosa na crianˋa: relato de caso

作者:Costa; Ana Lucia Frana da; Carvalho; Teresinha Castelo Branco; Sousa; Ana Virginia Lopes de
来源:Anais Brasileiros de Dermatologia, 2005.
DOI:10.1590/S0365-05962005000700006

摘要

mastocytosis is a rare disease, defined as a disorderly infiltration with mast cells in several tissues. it comprises many different clinical situations varying from indolent cutaneous forms to malignant and systemic conditions. the term bullous mastocytosis describes all the variety in which the cutaneous bullae represent the predominant feature and generally indicates cases of diffuse cutaneous mastocytosis. its presence is more common during the childhood and has a more reserved prognosis. this case report emphasizes the extreme diversity of its clinical manifestations and complications.

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