摘要
malignant chondroid syringoma (malignant mixed tumor of the skin) is an extremely rare tumor. approximately 40 cases have been described to date. it is a neoplasm originated from sweat gland. the tumor predominantly affects the trunk and distal extremities, arises in the sixth decade and shows a predilection for females. we relate one case with clinical and histopathologic typical features to alert the pathologist to this diagnosis, since this neoplasm has a metastasic rate of approximately 60% (lymph nodes, lungs and bones are predominantly affected) and a mortality of roughly 25%.