Inflammatory profile in X‐linked adrenoleukodystrophy patients: Understanding disease progression

作者:Desirèe Padilha Marchetti; Bruna Donida; Carlos Eduardo Jacques; Marion Deon; Tatiane Cristina Hauschild; Patricia Koehler‐Santos; Daniella de Moura Coelho; Adriana Simon Coitinho; Laura Bannach Jardim; Carmen Regla Vargas
来源:Journal of Cellular Biochemistry, 2018, 119(1): 1223-1233.
DOI:10.1002/jcb.26295

摘要

Abstract(#br)X‐linked adrenoleukodystrophy (X‐ALD) is an inherited disease characterized by progressive inflammatory demyelization in the brain, adrenal insufficiency, and an abnormal accumulation of very long chain fatty acids (VLCFA) in tissue and body fluids. Considering that inflammation might b...