Choroba czy zespó? Caroliego? Od zaburzeń embriogenezy do przeszczepienia w?troby

作者:Patryk Lipiński; Dorota Wicher; Piotr Kaliciński; Joanna Cielecka Kuszyk; Irena Jankowska
来源:Pediatria Polska, 2016, 91(5): 453-457.
DOI:10.1016/j.pepo.2016.04.003

摘要

Abstract(#br)Caroli's disease is a rare congenital disease of the liver characterized by multiple segmental cystic dilatation of intrahepatic bile ducts. The disease is referred as Caroli's syndrome when it is associated with congenital hepatic fibrosis. The clinical features include jaundice, right...

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