摘要
pulmonary langerhans%26apos;- cell histiocytosis belongs to a spectrum of diseases characterized by monoclonal proliferation and infiltration of organs by langerhans%26apos;cells. it is an uncommon interstitial lung disease of unknown etiology occurring almost exclusively in cigarette smokers. it%26apos;s course in adults is variable and unpredictable, ranging from benign self-limiting types with spontaneous regression to slowly progressive malignant disease that leads to respiratory failure and death. we report one patient diagnoses of pulmonary langerhans%26apos;cell histiocytosis who experimented an objetive radiographic improvement and disappearance of symptoms after smoking cessation.