摘要
incontinentia pigmenti is a rare x-linked genodermatosis that affects mainly female neonates. skin manifestations are the most common and occur in four quite distinct phases. a female infant presented vesiculobullous lesions on trunk and limbs, and a verrucous lesion on the right palm. biopsy revealed eosinophil exocytosis and pigment incontinence, confirming the clinical hypothesis. although uncommon, incontinentia pigmenti should be taken into consideration as a possible differential diagnosis when vesiculobullous and verrucous lesions are present in childhood.