Incontin那ncia pigmentar ligada ao X ou s赤ndrome de Bloch-Sulzberger: relato de um caso

作者:Pereira; Marcela A C; Mesquita; Lismary A de F; Budel; Anelise R; Cabral; Carolina S P; Feltrim; Amanda de S
来源:Anais Brasileiros de Dermatologia, 2010.
DOI:10.1590/S0365-05962010000300013

摘要

incontinentia pigmenti is a rare x-linked genodermatosis that affects mainly female neonates. skin manifestations are the most common and occur in four quite distinct phases. a female infant presented vesiculobullous lesions on trunk and limbs, and a verrucous lesion on the right palm. biopsy revealed eosinophil exocytosis and pigment incontinence, confirming the clinical hypothesis. although uncommon, incontinentia pigmenti should be taken into consideration as a possible differential diagnosis when vesiculobullous and verrucous lesions are present in childhood.

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