科研之友
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摘要
rosai-dorfman disease, otherwise known as sinus histiocytosis with massive lymphadenopathy, is a non-langerhans cell histiocytosis with a benign course and unknown etiology. it was described in 1969 as a painless cervical lymph node enlargement in association with fever, weight loss and sweating. extranodal disease has been reported in 43% of cases, with involvement of multiple organs. purely extranodal rosai-dorfman disease has been already reported, including forms restricted to the skin. this paper reports a case of purely cutaneous rosai-dorfman disease, which is of interest in view of the rarity of this condition.
