Pseudoporfiria induzida pela di芍lise tratada com N-acetilciste赤na oral

作者:Guiotoku; Marcelo Massaki; Pereira; Fabiola de Paula; Miot; Helio Amante; Marques; Mariangela Esther Alencar
来源:Anais Brasileiros de Dermatologia, 2011.
DOI:10.1590/S0365-05962011000200031

摘要

pseudoporphyria is a rare bullous dermatosis that clinically and histopathologically is similar to porphyria cutanea tarda. it mainly affects patients with chronic renal failure on peritoneal dialysis or hemodialysis. medications can also be involved in the etiology. diagnosis and management of this condition is a challenge for dermatologists. the authors report a case of pseudoporphyria related to dialysis with favorable outcome after the use of oral n-acetylcysteine.

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